Early myoclonic encephalopathy(EME) is an electroclinical entity which probably results from a genetic progressive disease and which occurs a few days or weeks after birth in a previously healthy bady; at onset it is associated with myoclonic
jerks,
partial clonic fits and periodic EEG aspects that afterwards evolve to a pattern wherein partial fits, spasms, and suppression-bursts coexist; within a few months it finally leads to a decerebrate state. We experienced of early myoclonic
encephalopathy
in a 3 month-old female patient, who had recurrent myoclonic attacks, marked delay of psychomotor development, and characteristic burst-suppression EEG pattern.
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